Beyond Hypoplastic Left Heart Syndrome: The Spectrum of Congenital Heart Disease Associated with Left Ventricular Hypoplasia
نویسندگان
چکیده
Left ventricular hypoplasia complicates other forms of congenital heart disease in addition to the classic ‘‘hypoplastic left heart syndrome.’’ Within this heterogeneous group, subtle anatomic differences determine surgical management and ultimate prognosis. Thus, an individualized approach is necessary to optimize outcomes in this complex population.
منابع مشابه
Holt-Oram Syndrome: A Rare Variant
Holt-Oram syndrome is an autosomal dominant disorder, characterised by skeletal abnormalities of the upper limb associated with congenital heart defect, mainly atrial and ventricular septal defects. Skeletal defects exclusively affect the upper limbs in the preaxial radial ray distribution and are bilateral and asymmetrical. They range from clinodactyly, absent or digitalised thumb, hypoplastic...
متن کاملThe nomenclature, definition and classification of hypoplastic left heart syndrome.
The hypoplastic left heart syndrome encompasses a spectrum of cardiac malformations that are characterized by significant underdevelopment of the components of the left heart and the aorta, including the left ventricular cavity and mass. At the severe end of the spectrum is found the combination of aortic and mitral atresia, when the left ventricle can be close to non-existent. At the mild end ...
متن کاملMonochorionic twins discordant for congenital heart disease: a referral center's experience and possible pathophysiologic mechanisms.
OBJECTIVE To describe the spectrum of cardiac defects in monochorionic (MC) twins discordant for congenital heart disease (CHD) in a referral center population. METHOD Retrospective study of all twin gestations undergoing echocardiography between 2000 and 2009 at our institution. RESULTS A total of 356 twin pairs were evaluated during the study period, 202 for suspected twin-twin transfusio...
متن کاملLeft heart hypoplasia with associated anomalies.
The malformed heart to be described was removed at necropsy from a 9-day old Bantu infant, and sent to the Department of Anatomy for study. Unfortunately neither the clinical nor necropsy records could subsequently be traced and the only information available was that the cause of death was thought to be partial atelectasis. The main vessels branching off the arterial trunk were identified for ...
متن کاملA Rare Association of Right-sided Congenital Diaphragmatic Hernia and Encephalocele: A Case Report
Background: This is a case report regarding a 2051-gram female newborn affected by right-sided congenital diaphragmatic hernia (CDH) presenting with encephalocele in the occipital region. Case report: The newborn was delivered by a 38-year-old mother from Darmian city, a rural district located in South Khorasan province, Iran. Co...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
دوره شماره
صفحات -
تاریخ انتشار 2013